Single Ventricle with Mitral and Aortic Atresia

نویسندگان

  • Vijaya V Mysorekar
  • Chitralekha P Dandekar
چکیده

Congenital cardiovascular malformations occur in about 5 to 8 of every 1,000 live births, and the percentage in stillborn infants is probably even higher. Between the 5 and 8 weeks of embryonic life, the primitive heart tube undergoes a process of folding, remodeling with the formation of valves, and septation that transforms its single lumen into the four chambers of the definitive heart. Although the cause and pathogenesis of most cardiovascular defects is not well understood, genetic errors, environmental teratogens or altered haemodynamic forces may be responsible in most cases.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Absence of the aortic valve cusps with mitral atresia, normal left ventricle, and intact ventricular septum.

A case of a previously unreported anomaly is presented in which absence of the aortic valve cusps, mitral atresia, a normal left ventricle, and an intact ventricular septum were diagnosed by cross sectional echocardiography. The development of a normal left ventricle, rather than the hypoplastic ventricle usually associated with mitral atresia, is explained by filling of the ventricular cavity ...

متن کامل

Aortic valve atresia with a normally developed left ventricle.

Aortic valve atresia is usually associated with hypoplasia of the left ventricle and mitral valve. We report a patient presenting aortic atresia with ventricular septal defect and a normally sized left ventricle. The electrocardiogram showed left axis deviation and left ventricular hypertrophy. The ventricular septal defect probably favored a normal growth of the left ventricle, allowing it to ...

متن کامل

Aortic atresia with normally developed left ventricle in a young adult.

Congenital aortic valve atresia is usually part of a developmental anomaly usually called 'hypoplastic left-heart syndrome'. To the best of our knowledge, most reported cases of aortic atresia have been associated with hypoplasia of the ascending aorta, of the left ventricle, and of the mitral valve. We report a patient presenting with aortic atresia with a ventricular septal defect and a norma...

متن کامل

Mitral Atresia with Normal Aortic Valve

Eighteen cases of mitral atresia with normal aortic valve plus 68 cases from the literature are analyzed. A new classification based on anatomical findings is proposed. Pulmonary stenosis or atresia is frequent in the type with transposition of the great arteries. The rare instances of normal or large left ventricle are due to a large ventricular septal defect, or to straddling or displaced tri...

متن کامل

Mitral Atresia with Normal Aortic Valve

Eighteen cases of mitral atresia with normal aortic valve plus 68 cases from the literature are analyzed. A new classification based on anatomical findings is proposed. Pulmonary stenosis or atresia is frequent in the type with transposition of the great arteries. The rare instances of normal or large left ventricle are due to a large ventricular septal defect, or to straddling or displaced tri...

متن کامل

The impact of anatomical subgroups for regional and global function of the right ventricle in hypoplastic left heart syndrome

Methods 36 children (5.8 ± 2.4 yrs) with HLHS after completion of Fontan-circulation were investigated. 17 patients (pts) had mitral and aortic atresia (MA/AA) without a visible left ventricular cavity. In 19 pts representing the anatomical subgroups mitral stenosis/aortic atresia (MS/AA) and mitral stenosis/aortic stenosis (MS/AS) a left ventricular cavity was present. We used CMR cine-imaging...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره   شماره 

صفحات  -

تاریخ انتشار 2006